Rehabilitación bucal bajo anestesia general en el Síndrome de Alagille. Reporte de un caso

Abstract

The Alagille syndrome is a multi-systemic disorder, it is inherited as an autosomal dominant trait, with variable clinical manifestations, mainly affects the liver, and biliary conduits, kidneys, heart, eyes, and an unusual butterfly shape of the bones of the spinal column. The estimated prevalence of Alagille syndrome is 1 in 100,000 live births. It is important to eliminate caries in the buccal cavity of these patients by the susceptibility to present infectious processes and sepsis by inherent immunological depression of the syndrome. This article describes the case of a patient with diagnosis of Alagille Syndrome and the multidisciplinary treatment to carry out the buccal rehabilitation under general anesthesia, it is important to inform that the patient presented complete green pigmentation of the primary dentition, because of the bilirubin, the treatment was radical for the elimination of infectious centers, putting in front the health of patient to the aesthetic one.